type I neurofibromatosis, peripheral type or classic cutaneous form. since puberty slowly increasing, soft, 0.2-0.8 cm large, skin-coloured or slightly brownish, painless, flat or hemispherical papules and nodules in a 42-year-old patient. the bell-button phenomenon can be triggered (the papules can be pressed into the skin under pressure). café-au-lait spots up to 7 cm in diameter also appear on the trunk.
Urticaria pigmentosa: about 0.5-1.0cm large, disseminated, oval or round, brownish-red spots. only when rubbed, increased reddening of the spots with accompanying itching. also during warm showers or baths increased reddening and clearly palpable elevation of the lesions. Darier phenomenon can be triggered (see neck on the right, here extensive reddening with slight itching, after rubbing this area).
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