Urticaria pigmentosa bullosaQ82.2

Author:Prof. Dr. med. Peter Altmeyer

All authors of this article

Last updated on: 19.11.2021

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Synonym(s)

Urticaria pigmentosa pemphigoides

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DefinitionThis section has been translated automatically.

Rare form of cutaneous mastocytosis with vesicular reaction in the area of pigmented efflorescences to physical stimuli. Internal manifestations are possible(mastocytosis).

ManifestationThis section has been translated automatically.

Especially infants and small children are affected.

Clinical featuresThis section has been translated automatically.

Itching, rubbing, urticarial reaction with blistering, long-standing hyperpigmentation.

Differential diagnosisThis section has been translated automatically.

Epidermolysis bullosa group.

General therapyThis section has been translated automatically.

According to Urticaria pigmentosa, see there.

External therapyThis section has been translated automatically.

Dry brushing with disinfecting solutions such as potassium permanganate (light pink) or quinolinol (e.g. Chinosol 1:1000 or R042 ). In case of severe itching, creams or lotions containing glucocorticoids with 0.5-1.0% hydrocortisone R119, R123 or 0.05-0.1% betamethasone R030 for a short time.

Internal therapyThis section has been translated automatically.

S.u. Urticaria pigmentosa.

LiteratureThis section has been translated automatically.

  1. Fenske NA et al (1985) Congenital bullous urticaria pigmentosa. Arch Dermatol 121: 115-118
  2. Has C et al (2002) Recurring staphylococcal scalded skin syndrome-like bullous mastocytosis: the utility of cytodiagnosis and the rapid regression with steroids. Pediatric Dermatol 19: 220-223
  3. Haustein UF et al (1997) Bullous mastocytosis in a child. dermatologist 48: 127-129
  4. Stanka F et al (1984) Urticaria pigmentosa bullosa. Nude Dermatol 10: 166-168
  5. Valent P et al (2003) Mast cell proliferative disorders: current view on variants recognized by the World Health Organization. Hematol Oncol Clin North Am 17: 1227-1241

Authors

Last updated on: 19.11.2021

Author: Prof. Dr. med. Peter Altmeyer