Lymphedema, type meigeQ82.0
Synonym(s)
late-onset; lymphedema; Lymphedema; lymphedema late-onset; lymphedema praecox familial; Maladie de Meige; Meige's disease; Meige\'s disease; Meige syndrome; Trophodema; Trophodema type Meige; Type Meige
HistoryThis section has been translated automatically.
Meige, 1889
DefinitionThis section has been translated automatically.
Genetically determined primary lymphedema corresponding to lymphedema, type Nonne-Milroy with further associated symptoms and later manifestation
EtiopathogenesisThis section has been translated automatically.
Unknown.
ManifestationThis section has been translated automatically.
Puberty. Women are affected twice as often as men.
Clinical featuresThis section has been translated automatically.
- According to the lymphedema, type Nonne-Milroy, s. there.
- In addition: short stature, mental retardation, hypogenitalism, ptosis of the eyelids, recurrent intrahepatic cholestasis, obesity in the area of the breeches; rarely additional infestation of the genitals, upper extremities, face, larynx and pleura (effusions).
- Congenital anomalies: partial membranous syndactylia of the toes, distichiasis (double row of eyelashes); myopia; ptosis; yellow nails; extradural cysts and/or vertebral anomalies; cerebrovascular malformations; sensoneural hearing loss; cleft palate. Bronchiectasis.
TherapyThis section has been translated automatically.
LiteratureThis section has been translated automatically.
- Figueroa AA, Pruzansky S, Rollnick BR (1983) Meige disease (familial lymphedema praecox) and cleft palate: report of a family and review of the literature. Cleft palate J 20: 151-157
- Meige H (1898) Dystrophy oedematose hereditaire. La presse médicale (Paris) 6: 341-343
- Meige H (1889) Le trophoedème chronique héréditaire. Nouv iconogr Salpêtrière, Paris, 12: 453-480
- Ho WL et al (2003) Radiological features of late-onset lymphoedema in Noonan's syndrome. Pediatric radiol 33: 200-202
- Samlaska CP (2002) Congenital lymphedema and distichiasis. Pediatric Dermatol 19: 139-141
- Tammer ME et al (2002) Surgical therapy of scrotal edema in elephantiasis congenita hereditaria (Meige type). Urologist A 41: 493-495
- Wheeler ES et al (1981) Familial lymphedema praecox: Meige's disease. Plast Reconst Surgery 67: 362-364