Arteriovenous malformationD18.0

Author:Prof. Dr. med. Peter Altmeyer

All authors of this article

Last updated on: 06.08.2021

Dieser Artikel auf Deutsch

Synonym(s)

Acral arteriovenous tumor; angioma racemosum; arteriovenous malformation; Arterivenous malformation; Aterio-venous; AVM; haemangioma racemosum; Haemangioma racemosum; Malformation; tendral angioma

Requires free registration (medical professionals only)

Please login to access all articles, images, and functions.

Our content is available exclusively to medical professionals. If you have already registered, please login. If you haven't, you can register for free (medical professionals only).


Requires free registration (medical professionals only)

Please complete your registration to access all articles and images.

To gain access, you must complete your registration. You either haven't confirmed your e-mail address or we still need proof that you are a member of the medical profession.

Finish your registration now

DefinitionThis section has been translated automatically.

Rare, congenital malformation of arterial and venous vessels with formation of arteriovenous anastomoses, a consecutive hypertensive varicosis. In principle, AVM can occur in any organ (e.g. cerebral, pulmonary, spinal, musculature) and will cause different symptoms depending on its location. The skin can be directly or indirectly involved. Not uncommon are capillary malformations (naevus flammeus) with/without varicosis, or an isolated varicosis without capillary skin involvement in combination with arterioverous shunts of the subcutis or muscles. AVMs are mostly a therapeutic indication due to their hemodynamic effects and progression tendency (no tumor occurrence, the name hemangioma is not justified).

ClassificationThis section has been translated automatically.

Stage I (clinical latency): Detection of AV shunts by Doppler sonography; skin lesions (nevus flammeus) may be present.

Stage II: Always detect AV shunts by Doppler sonography; skin lesions (flammeous nevus) with large caliber veins.

Stage III: Destructive tissue changes on the skin, in the subcutis or the musculature.

Stage IV (stage of decompensation): Venous hypertension with increased cardiac load (increased shunt volume). Signs of advanced venous insufficiency of the skin.

ManifestationThis section has been translated automatically.

Occurs from birth or in earliest youth, preferably in boys.

LocalizationThis section has been translated automatically.

Lower leg, complete leg, almost always hemiplegic; hands, face, skin involvement (nevus flammeus, varicosis) is not obligatory.

Clinical featuresThis section has been translated automatically.

About 2-4 mm in size, but also blue-red, symptomless spots, papules and plaques. Sometimes pulsating or buzzing, protruding, blue-red vessels. A combination with other malformations is possible. The surface is usually smooth, but can also be verrucous.

HistologyThis section has been translated automatically.

Collection of small, differently calibrated, thick-walled (venous) vessels. Broad fibromuscular vessel walls with elastic fibres, single-layer endothelial lining of the vessels. Also incisions of smaller arterioles.

Complication(s)This section has been translated automatically.

Possible development of skeletal changes, restricted movement, pain dependent on movement.

TherapyThis section has been translated automatically.

Radiation refractory, if necessary surgery or catheter-based embolization. The decisive factor is the elimination of the so-called nidus, which is the site of the short-circuit connection between the artery and the often aneurysmatically dilated drainage vein. The sole embolization of the incoming artery without reaching the actual nidus should be avoided. Absolute 96% alcohol with a coiling of the nidus has proven to be the most effective therapy.

LiteratureThis section has been translated automatically.

  1. Kutzner H (2003) Vascular tumors of the skin. In: Kerl H et al (Ed.) Histopathology of the skin. Springer Publishing House, Berlin Heidelberg New York, S. 763
  2. Yang CH, Ohara K (2002) Acquired digital ateriovenous malformation: a report of three cases annd study with epiluminescence microscopy. Br J Dermatol 147: 1007-1009

Authors

Last updated on: 06.08.2021