Angioma serpiginosum L81.7

Rare, superficial, nevoidal vascular neoplasms, occurring predominantly in girls (during puberty) and young women (relapses during pregnancy possible).

Occasionally associations with systemic diseases have been described (Sjögren's syndrome, primary biliary cirrhosis, paraproteinemia), without a pathogenetic explanation for these comorbidities.

Gynecotropy: Women are affected about 9 times more often than men.

Unknown.

Mostly occurring in childhood (80% of patients are affected before the age of 18). Rarely present at birth.

Disseminated, 1-2 mm in size, bright red to purple-coloured, sometimes non-removable, dot-shaped spots. Occasionally also telangiectasias. Serpiginous, gyrated or linear patterns are produced by grouped arrangement. Occurring on one or both sides (rather symmetrical). Palms, soles and the mucous membranes close to the skin remain free.

Manifestations along the Blaschko lines are rarely described.

Convolute dilated capillaries with or without thickening of the vessel wall in the papillary stratum, sometimes also capillary proliferation and erythrocyte extravasations. No inflammatory infiltrates.

Laser therapy(e.g. pulsed dye laser) can be applied with good results.

Alternative: diathermy needle sclerotherapy.

Supplementary: cosmetic cover.

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