Angiodysplasia Q87.8

Generic term for all mono- or polyorganic, mono- or polytopic vascular malformations(= vascular malformations) as a result of abnormal embryonic tissue development. Always benign course, no signs of atypia or anaplasia. These benign vascular malformations can affect veins, arteries and lymph vessels separately or in combination.

Epidermiological data are unreliable. Estimates are at incidences of 1.2-1.5% of newborns. The incidence of angiodysplasia decreases from peripheral vessels via central vessels to visceral vessels.

Remember! The term "vascular malformation", increasingly used in the Anglo-American language area, is synonymous with angiodysplasia. Often the malformation is specified by the adjectives "venous, lymphogenic or arterial" malformation.

There are a number of attempts to systematize angiodysplasia, which have not been very satisfactory so far.

• Schobinger classification
• Hamburg Classification
• ISSVA Classification
• Classification according to Mulliken and Glowacky

1. NüllenH et al (2010) Varicosis in angiodysplasia. In: T Noppeney, H Nüllen Diagnosis and therapy of varicosis. Springer Medicine Publishing House Heidelberg S 158 -169
2. Prave F et al (2003) Vascular manifestation of von Recklinghausen neurofibromatosis: case report of venous dysplasia. Vasa 32: 36-39
3. Wilcken DE (2003) Overview of inherited metabolic disorders causing cardiovascular disease. J Inherited metab Dis 26: 245-257
4. Wolf C, Partsch H (1987) Angiodysplasias of the extremities. dermatologist 38: 645-651