Jones G 1977
Jones syndromeH 90.3
HistoryThis section has been translated automatically.
DefinitionThis section has been translated automatically.
Very rare, hereditary (autosomal-dominant inheritance) but also sporadically occurring disease characterized by gingival fibromatosis and a progressive sound sensitivity disorder (Gita S et al. 2014).
Occurrence/EpidemiologyThis section has been translated automatically.
Prevalence is given as < 1: 1,000,000. So far, two families have been described over several generations ( Jones RS et al. 1977).
Clinical featuresThis section has been translated automatically.
Slow fleshy hyperplasia of the gingiva that begins with the appearance of permanent teeth. Possible displacement of teeth. Gradual reduction of hearing.
LiteratureThis section has been translated automatically.
- Gita S et al (2014) Idiopathic gingival fibromatosis associated with progressive hearing loss: A nonfamilial variant of Jones syndrome. Contemporary clinical dentistry 5: 260-263.
- Jones RS et al (1977) Familial gingival fibromatosis associated with progressive deafness in five generations of a family. Birth defects original article series. 13: 195–201.