Dysodontic leukotrichosis-capitis-sanguinatio syndromeQ18.8
Synonym(s)
DLS; DLS Syndromes; Dysodontia, leucotrichosis capitis-sanguinatio; Dysodontia Leucotrichosis capitis-Sanguinatio
DefinitionThis section has been translated automatically.
Probably autosomal dominant inherited hypotrichotic ectodermaldysplasia
with:
- tooth anomalies hyperdontia in the canine region, enamel defects, positional anomalies
- Premature graying of the hair beginning in adolescence
- Normal pigmentation of the eye hair and secondary hair
- Gastrointestinal bleeding and epistaxis
- Hypohidrosis
- Abnormal brittleness of finger- and toenails
LiteratureThis section has been translated automatically.
- Weyers H. (1971) A new complex of ectodermal dysplasia: dysodontia, leucotrichosis capitis-sanguinatio (DLS-syndrome)]. Dental practice 22:286-288.