Cholangitis primary sclerosing K83.0

Author: Prof. Dr. med. Peter Altmeyer

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Last updated on: 29.10.2020

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Synonym(s)

PSC

Definition
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Sclerosing chronic inflammation of the extra- and intrahepatic bile ducts with consecutive destruction of the bile ducts.

Occurrence/Epidemiology
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Prevalence 1:100,000 per year

Etiopathogenesis
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Unresolved

Manifestation
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Increased occurrence between the 30-50 LJ;

Clinical features
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In the early stages asymptomatic. Later unclear upper stage symptoms, weight loss, icterus, itching.

The disease is more often than not accompanied by "chronic inflammatory bowel disease" (CED), usually ulcerative colitis. Furthermore, an association with the Sjögren's syndrome is found.

Laboratory
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Increased cholestasis parameters; frequent (60%) detection of ANA and ANCA (p-ANCA).

Disclaimer

Please ask your physician for a reliable diagnosis. This website is only meant as a reference.

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Last updated on: 29.10.2020