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Unilateral naevoid telangiectasia syndromeI78.8

Author:Prof. Dr. med. Peter Altmeyer

Last updated on: 12.05.2024

Synonym(s)

acquired nevoid telangiectasia; Nevoidal telangiectasia syndrome; Spider naevi unilateral; Teleangiectasia naevoide unilateral; Teleangiectasia unilateral; unilateral dermatomal superficial teleangiectasia; Unilateral naevoid telangiectasias; unilateral nevoidal telangiectasia; Unilateral nevoid telangiectasia syndrome; unilateral nevoid teleangiectasia; unilateral Spider Naevi; unilateral telangiectasia; UNTS

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HistoryThis section has been translated automatically.

Mazereeuw-Hautier 2003

DefinitionThis section has been translated automatically.

Extensive, unilateral, either congenital or acquired districts with dense telangiectasias.

EtiopathogenesisThis section has been translated automatically.

Unknown, often estrogen-induced manifestation. A genetically fixed, increased number of estrogen or progesterone receptors in the affected vessels is discussed.

ManifestationThis section has been translated automatically.

Occurs mainly during pregnancy, puberty and alcohol-related liver diseases. Rarely present congenitally.

LocalizationThis section has been translated automatically.

Preferably face, neck, shoulder-arm region, but also lower extremity and trunk. The arrangement of the lesions largely follows the dermatomes (trigeminal region,_C3,_C4, thoracic dermatomes, etc.)

Clinical featuresThis section has been translated automatically.

Discrete or pronounced, usually sharply defined erythema, composed of fine and very fine, often star-shaped branched telangiectasias, which largely disappear under glass spatula pressure. No involvement of internal organs or the CNS. No endocrinopathies in congenital forms. Quadrant and hemiplegic formations as well as appearances along the Blaschko lines are possible.

HistologyThis section has been translated automatically.

Dermal vasculature.

Differential diagnosisThis section has been translated automatically.

Nevus flammeus; Bloom syndrome; Ataxia teleangiectatica; Teleangiectasia hereditaria haemorrhagica; Nevus anaemicus; Nevus teleangiectaticus; essential teleangiectasia; Angioma serpiginosum; Teleangiectasia macularis eruptiva perstans.

TherapyThis section has been translated automatically.

Laser treatment with argon or pulsed dye laser leads to improvement of clinical symptoms.

Progression/forecastThis section has been translated automatically.

The intensity of the skin changes usually decreases after the hormonal changes. Nodular transformation as in the naevus flammeus is not likely.

LiteratureThis section has been translated automatically.

Abeck D et el. (1992) Unilateral naevoidal telangiectasia syndrome case observation and literature review. Z Hautkr 67: 688-690
Raff M et al (1982) Unilateral nevoidal telangiectasia syndrome. Dermatologist 33: 148-151
Sardana K et al (2001) Unilateral nevoid telangiectasia syndrome. J Dermatol 28: 453-454
Uhlin SR et al (1983) Unilateral nevoid telangiectatic syndrome. The role of estrogen and progesterone
receptors. Arch Dermatol 119:226-228.
Wilkin JK et al (1983) Unilateral dermatomal superficial teleangiectasia. J Am Acad Dermatol 8: 468-477
Wollina U et al (2001) Acquired nevoid telangiectasia. Dermatology 203: 24-26

Authors

Last updated on: 12.05.2024

Author: Prof. Dr. med. Peter Altmeyer