Plaque-like form of cutaneous mucinosis L98.5

Harald Otto Perry, 1960

Chronic cutaneous mucinosis (and oral mucosa) with dense, reddened, otherwise asymptomatic papules and plaques.

Face, trunk, oral mucosa.

There are 2.0 to 10.0 cm large or even larger, single or multiple, red, mostly asymptomatic, moderately indurated, non-scaly plaques, which show a punctured, follicle accentuated surface (peau d`orange). In contrast to the so-called mucinosis follicularis or keratosis pilaris, the follicular structure does not appear by itself, but secondary to the deposition of mucin into the interfollicular tissue.

Remark: The clinical description of this clinical picture is similar to the REM syndrome, which was highlighted again 14 years later by Gerd-Klaus Steigleder. It is discussed whether both terms are not synonymous terms for the same entity.

1. Bharti V et al (2012) Oral focal mucinosis of palatal mucosa: A rare case report. Contemp Clin Dent 3(Suppl 2):S214-218
2. Carrington PR et al (1998) Plaque-like erythema with milia: a noninfectious dermal mucinosis mimicking cryptococcal cellulitis in a renal transplant recipient. J Am Acad Dermatol 39(2 Pt 2): 334-337
3. Gutte R et al (2012) Asymptomatic nodule over the skin. Cutaneous focal mucinosis (CFM). Indian J Dermatol Venereol Leprol 78:123
4. Kaufmann R et al (1998) Dermatomyositis presenting as plaque-like mucinosis. Br J Dermatol 138: 889-892
5. Perry HO, Kierland RR, Montgomery H (1960) Plaque-like form of cutaneous mucinosis. Arch Dermatol 82: 980-985
6. Yamamoto M et al (2011) Plaque-type cutaneous focal mucinosis. Int J Dermatol 50:896-898