Papillomatosis cutis lymphostatica I89.0

Polysymptomatic dermatological manifestation of a chronic lymphedema (mainly of the distal and proximal extremities, less frequently on abdominal aprons and mammae) with formation of skin-coloured to dirty brown, extensive, indurated, verrucous skin changes. In rare cases grotesque pseudotumorous vegetation may also occur.

Mostly secondary disease resulting from disturbances in regional subcutaneous lymph drainage, e.g. chronic venous insufficiency, obesity and heart failure, primary lymphedema, chronic recurrent erysipelas, after extirpation of the inguinal and/or iliac lymph nodes with or without subsequent radiation, lymphatic filiariosis, chronic podoconiosis.

Lower extremity, more rarely upper extremity, in amputation stumps, in abdominal folds in obesity permagna and the resulting lymph congestion.

• Therapy of a possibly existing stasis oedema in chronic venous insufficiency (CVI).
• Therapy of lymphedema by means of compression therapy and manual and, if necessary, intermittent lymphatic drainage.
  Change of lifestyle to targeted sporting activities (cycling, hiking, swimming) and, if necessary, elimination of obesity. Consistent prophylaxis of infections with secondary lymphedema.

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2. Lindemayr H (1988) Therapy successes with urea-containing topicals in papillomatosis cutis verrucosa (lymphostatic congestive papillomatosis) Dermatologist 39: S78-79
3. Niederauer HN et al (1991) tumor form of a papillomatosis cutis lymphostatica. Dermatologist 42: 518-522
4. Stöberl C et al (1988) Lymphostatic stasis dermatosis. Dermatologist 39: 441-446
5. Vaccaro M et al (2000) Elephantiasis nostras verrucosa. Int J Dermatol 39: 764-766