Onychodysplasia congenital of the index fingerQ84.6

Author:Prof. Dr. med. Peter Altmeyer

All authors of this article

Last updated on: 27.11.2022

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Synonym(s)

congenital ischemic onychodystrophy; congenital onychodysplasia; Congenital syndrome of the index finger; Iso-Kikuchi Syndrome; Onychodystrophy congenital ischemic

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HistoryThis section has been translated automatically.

Iso, 1969; Kikuchi, 1974

DefinitionThis section has been translated automatically.

Rare, congenital, very variable nail dysplasia, mainly of the index finger, often associated with bony changes of the end phalanx.

EtiopathogenesisThis section has been translated automatically.

Unsolved. Discussed are autosomal dominant inheritance, medication during pregnancy, atavism.

LocalizationThis section has been translated automatically.

Predominantly occurring on the index finger. Localization on other fingers is possible. Toes are rarely affected. Infestation on one or both sides is possible.

Clinical featuresThis section has been translated automatically.

Mostly microonychia or polyonychia, less frequently onychogrypose. Radiological narrowing of the distal phalanx, dorsal spur formation at the distal phalanx.

Differential diagnosisThis section has been translated automatically.

Aplasia cutis congenita; syndactyly and polydactyly; nail-patella syndrome; anhidrotic ectodermal dysplasia; dyskeratosis congenita; epidermolysis bullosa group.

TherapyThis section has been translated automatically.

The disease is harmless; no causal therapy is known.

LiteratureThis section has been translated automatically.

  1. Bittar EO et al (1988) Congenital ischemic onychodystrophy (Iso-Kikuchi syndrome) and chronic lupus erythematosus. Dermatologist 39: 750-752
  2. Haneke E et al (1984) Congenital onychodysplasia: Iso-Kikuchi syndrome. dermatologist 35: 468-471
  3. Iso R (1969) Congenital nail defects of the index finger and reconstructive surgery. Seikei Geka 20: 1383-1384
  4. Kikuchi I, Horikawa S, Amano F (1974) Congenital onychodysplasia of the index fingers. Arch Dermatol 110: 743-746
  5. Thappa DM et al (2002) Polyonychia in congenital onychodysplasia of the index finger (Iso and Kikuchi syndrome): a report from India. J Dermatol 29: 603-605

Authors

Last updated on: 27.11.2022

Author: Prof. Dr. med. Peter Altmeyer