Lipoid proteinosis in photosensitivityE80.0

Author:Prof. Dr. med. Peter Altmeyer

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Last updated on: 29.10.2020

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Synonym(s)

Light-induced lipoid proteinosis; Lipoid proteinosis light-induced

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HistoryThis section has been translated automatically.

Urbach and Wiethe, 1929

DefinitionThis section has been translated automatically.

Today no longer commonly used term for skin symptoms in extremely light-sensitive patients with protoporphyria erythropoetica, with a clinical aspect reminiscent of hyalinosis cutis et mucosae.

ManifestationThis section has been translated automatically.

Especially in spring.

LocalizationThis section has been translated automatically.

Skin areas exposed to light.

Clinical featuresThis section has been translated automatically.

Patchy papuloverrucous changes on the sides and edges of the fingers, on the elbows, in the nose area. No mucous membrane changes, no involvement of internal organs.

DiagnosisThis section has been translated automatically.

S.u. Protoporphyria erythropoetica.

Differential diagnosisThis section has been translated automatically.

Hyalinosis cutis et mucosae

TherapyThis section has been translated automatically.

S.u. Protoporphyria erythropoetica.

LiteratureThis section has been translated automatically.

  1. Findlay GH (1987) Lipoid proteinosis. In: Fitzpatrick TB, Eisen AZ, Wolff K, Freedberg IM, Austen KF (eds) Dermatology in General Medicine. McGraw-Hill New York St. Louis San Francisco, pp 1760-1763
  2. Hamada T et al (2003) Extracellular matrix protein 1 gene (ECM1) mutations in lipoid proteinosis and genotype-phenotype correlation. J Invest Dermatol 120: 345-350
  3. Hamada T (2002) Lipoid proteinosis. Clin Exp Dermatol 27: 624-629
  4. Ko C et al (2003) Vesicular lesions in a patient with lipoid proteinosis: a probable acantholytic dermatosis. Am J Dermatopathol 25: 335-337
  5. Nanda A et al (2001) Lipoid proteinosis: report of four siblings and brief review of the literature. Pediatric Dermatol 18: 21-26
  6. Oyama N et al (2003) Autoantibodies to extracellular matrix protein 1 in lichen sclerosus. Lancet 362: 118-123
  7. Sethuraman G et al (2003) Lipoid proteinosis in two siblings: a report from India. J Dermatol 30: 562-365
  8. Urbach E, Wiethe C (1929) Lipoidosis cutis et mucosae. Virchows Arch A Pathol Pathol Anat 273: 285-319

Authors

Last updated on: 29.10.2020

Author: Prof. Dr. med. Peter Altmeyer