Ichthyosis hystrix gravior, type lambertQ80.8
Synonym(s)
Porcupine People
DefinitionThis section has been translated automatically.
Autosomal dominant inherited spiky hyperkeratoses covering the entire body with the exception of the face, genitals, palmae and plantae. Only a few cases have been described so far.
External therapyThis section has been translated automatically.
Experimental Tazarotene locally. It should be noted that no more than about 2% of the skin surface should be treated simultaneously. S.u. Ichthyosis vulgaris, autosomal dominant.
Internal therapyThis section has been translated automatically.
No specific therapy known. Therapy trial with Acitretin (Neotigason) possible.