Hypertrichosis lanuginosa congenita Q84.2

Rare, generalized, autosomal dominant inherited, congenital, increased body hair, which is monoorganically limited to the integument, but also appears together with other organ involvement.

The dermatological findings are as follows: fine, non-markless, light to silver-grey hairs of up to 20 cm in length are found all over the body.

Only shaving or epilating by means of laser techniques can be considered.

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3. Chen W et al (2015) Congenital generalized hypertrichosis terminalis: a proposed classification and a plea to avoid the ambiguous term "Ambras syndrome". Eur J Dermatol 25:223-227.
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5. Salas-Alanis JC et al (2014) Hypertrichosis lanuginosa congenita treated with diode laser epilation during infancy. Pediatric Dermatol 31:529-530.
6. Shah IH et al. (2018) Congenital hypertrichosis lanuginosa. Indian J Dermatol Venereol Leprol 84:248.