Hemosiderotic fibrolipomatous tumor D36.1

Marshall-Taylor C et al. 2000

Very rare, locally aggressively growing, postoperatively often recurrent (dignity?), but not metastasizing, mesenchymal tumor whose entity seems not yet consolidated. The demarcation to the "myxoinflammatory fibroblastic sarcoma" with common cytogenetic features is not yet clear

Preferably infants, but also occurs in older age. Female persons seem to be more frequently affected.

Back of hands and feet, lower extremity, occasionally also in the face.

Uncharacteristic, 0.1-1.3 cm large (larger lesions also possible), subcutaneously localized, skin-colored or blue-atropical plaque, which may resemble an older hematoma. Nodules form less frequently.

Colorful image with fascicles of fibroblastically differentiated, CD34-positive spindle cells (negative for smooth muscle actin and desmin) with injected islets of mature adipocytes, hemosiderin-storing macrophages and multinucleated, osteoclast-like giant cells. Mitoses are rare.

Operatively with sufficient (histologically safe) safety margin.

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