DefinitionThis section has been translated automatically.
Circumscript scleroderma of one half of the face with encroachment on soft tissue and bone.
ManifestationThis section has been translated automatically.
Often occurring in childhood and adolescence.
Clinical featuresThis section has been translated automatically.
Initial edema, later sclerosis (difference to Hemiatrophia faciei progressiva) of a skin area on one side of the face or the whole half of the face, possibly infestation of soft tissues and bones with deformation.
TherapyThis section has been translated automatically.
The therapy approaches usually come too late. In the stage of sclerosing inflammation: trial with high-dose penicillin G (10 million IU/day i.v.), combination with UVA1 irradiation (40-60 J/cm2; total dose at 1200 J/cm2), correction of facial deformities by plastic surgery (e.g. fat implantation) in the burned-out stage. S.a.u. scleroderma, circumscripts.
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Please ask your physician for a reliable diagnosis. This website is only meant as a reference.
Prof. Dr. med. Peter Altmeyer