Haber`s syndromeQ82.84
Synonym(s)
Dermatosis familial rosacea-like with intraepidermal epitheliomas keratotic plaques and scars; Familial rosacea-like dermatosis with intraepithelial epitheliomas, keratotic plaques and scars; Haber`s syndromes
HistoryThis section has been translated automatically.
Haber 1965
DefinitionThis section has been translated automatically.
Rare, probably autosomal dominant inherited genodermatosis with rosacea-like, burning erythema on the face, possibly also brown pigmentation and induration.
ManifestationThis section has been translated automatically.
Childhood.
Clinical featuresThis section has been translated automatically.
Rosacea-like skin symptoms with flus response, telangiectasia, pustules, small scars, verruziform papules and nodules, especially dense in the armpits, hyperkeratotic foci on knees and elbows during and after adolescence.
Differential diagnosisThis section has been translated automatically.
TherapyThis section has been translated automatically.
Symptomatic rosacea therapy.
Salicylic acid-containing creams or oils for hyperkeratotic areas as well as prophylactic light protection agents (e.g. Anthelios, Eucerin Sun).
Note(s)This section has been translated automatically.
Since there have been no further publications on this syndrome in the last 20 years, the entity of the syndrome must be questioned. The extent to which there is a relationship to the disease described by Dowling-Degos or to dyschromatosis symmetrica hereditaria is currently not clear (McCormack CJ et al. 1997).
LiteratureThis section has been translated automatically.
- Binet O et al (1986) Haber's syndrome. Period French familiy (2 cases). Ann Dermatol Venerol 113: 43-50
- McCormack CJ et al (1997) Haber's syndrome. Australas J Dermatol 38:82-44.