Synonym(s)
infantile desmoid fibromatosis; Infantile desmoid-like fibromatosis
DefinitionThis section has been translated automatically.
A type of tumor belonging to the infantile fibromatoses, in which the tumor masses are located in the deep dermis and/or in the fascia or adjacent mucosa.
LocalizationThis section has been translated automatically.
Shoulder girdle, thighs, head and neck.
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Clinical featuresThis section has been translated automatically.
Thick, not tolerated, little movable, firm knots, which are usually discovered by chance.
DiagnosisThis section has been translated automatically.
Histology.
Differential diagnosisThis section has been translated automatically.
Fibrosarcoma (clinical and histological).
TherapyThis section has been translated automatically.
A sufficiently performed excision in healthy subjects is recommended. Risk of recurrence > 50%.
LiteratureThis section has been translated automatically.
- Kaçar A et al (2012) Childhood fibroblastic and myofibroblastic tumors: a multicenter documentation and review of the literature.Turk Patoloji Derg 28:24-30.
- Pilz T et al (1999) Chemotherapy in fibromatoses of childhood and adolescence: results from the Cooperative soft tissue sarcoma study (CWS) and the Italian Cooperative study group (ICG-AIEOP)]. Clinic Padiatr 211:291-295.
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Outgoing links (1)
Fibromatoses (overview);Disclaimer
Please ask your physician for a reliable diagnosis. This website is only meant as a reference.
Prof. Dr. med. Peter Altmeyer