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Fibromatosis digital infantileM72.8

Authors:Prof. Dr. med. Peter Altmeyer, Alexandros Zarotis

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Last updated on: 29.10.2020

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Synonym(s)

desmoid fibromatosis; Digital Fibroma recurrent; digital fibrous swellings in children; Fibroma infantile digital; Inclusion body fibromatosis; Infantile digital fibroma; juvenile aponeurotic fibroma; Keloid fibromatosis; recurrent digital fibroma; recurrent digital fibromatosis of childhood; Recurrent digital fibromatosis of childhood; recurring digital fibrous tumor of childhood

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HistoryThis section has been translated automatically.

Franck, 1908; Reye, 1965

DefinitionThis section has been translated automatically.

Rare, benign, myofibroblastically differentiated tumour on fingers or toes in infants and small children, with a tendency to infiltrative growth. Very rare in adults.

ManifestationThis section has been translated automatically.

Congenital (approx. 30% of cases), occurring shortly after birth or in the first months of life, or more rarely acquired later.

LocalizationThis section has been translated automatically.

Dorsal or lateral side of fingers or toes (except thumbs and big toes)

Clinical featuresThis section has been translated automatically.

Mostly single, more rarely multiple, coarse, flat to spherical, 1-2 cm large, reddish, cutaneous to subcutaneously located nodes.

HistologyThis section has been translated automatically.

Fuzzily defined, moderately cell-rich tumor parenchyma arranged in vertebrae and fascicles, whose spindle cells are partially oriented perpendicular to the epidermis. The tumor cells have a poorly delimited, moderately eosinophilic cytoplasm with eosinophilic inclusion bodies. They react positively with desmin and alpha-smooth muscular actin.

TherapyThis section has been translated automatically.

Leading total excision in sano without safety distance. Recurrences occur in up to 60% of cases. Spontaneous healing is possible.

LiteratureThis section has been translated automatically.

  1. Hügel et al (1995) Fibromatoses and other fibroblastically/myofibroblastically differentiated connective tissue tumors from the dermatologist's point of view. Z Hautkr 70: 717-724
  2. Kanwar AJ et al (2002) Congenital infantile digital fibromatosis. Pediatric Dermatol 19: 370-371
  3. Kawaguchi M et al (1998) A case of infantile digital fibromatosis with spontaneous regression. J Dermatol 25: 523-526
  4. Reye RDK (1965) Recurring digital fibrous tumor of childhood. Arch pathogen 80: 228-231
  5. Sarma DP, Hoffmann EO (1980) Infantile digital fibroma-like tumour in an adult. Arch Dermatol 116: 578-579

Authors

Last updated on: 29.10.2020

Authors: Prof. Dr. med. Peter AltmeyerAlexandros Zarotis