Congenital deficiency of leukocyte-adherence glycoproteinD84.9

Author:Prof. Dr. med. Peter Altmeyer

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Last updated on: 29.10.2020

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Synonym(s)

CDLG

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DefinitionThis section has been translated automatically.

Congenital immune defect with disturbed leukocyte function and tendency to infection.

Clinical featuresThis section has been translated automatically.

Pyoderma gangraenosum, skin necrosis, ulcerations, impaired wound healing, gingivitis, stomatitis, otitis media, pneumonia, etc.

TherapyThis section has been translated automatically.

No causal therapy known. Symptomatic treatment of the skin changes and infections.

Progression/forecastThis section has been translated automatically.

30% lethality.

LiteratureThis section has been translated automatically.

  1. Bedlow AJ et al (1998) Pyoderma gangrenosum in a child with congenital partial deficiency of leucocyte adherence glycoproteins. Br J Dermatol 139: 1064-1067
  2. Kerkhof PCM, Weemaes CMR (1990) Skin manifestation in congenital deficiency of leukocyte-adherence glycoprotein (CDLG). Br J Dermatol 123: 395-401

Authors

Last updated on: 29.10.2020

Author: Prof. Dr. med. Peter Altmeyer