Synonym(s)
CDLG
DefinitionThis section has been translated automatically.
Congenital immune defect with disturbed leukocyte function and tendency to infection.
Clinical featuresThis section has been translated automatically.
Pyoderma gangraenosum, skin necrosis, ulcerations, impaired wound healing, gingivitis, stomatitis, otitis media, pneumonia, etc.
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TherapyThis section has been translated automatically.
No causal therapy known. Symptomatic treatment of the skin changes and infections.
Progression/forecastThis section has been translated automatically.
30% lethality.
LiteratureThis section has been translated automatically.
- Bedlow AJ et al (1998) Pyoderma gangrenosum in a child with congenital partial deficiency of leucocyte adherence glycoproteins. Br J Dermatol 139: 1064-1067
- Kerkhof PCM, Weemaes CMR (1990) Skin manifestation in congenital deficiency of leukocyte-adherence glycoprotein (CDLG). Br J Dermatol 123: 395-401
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Cdlg;Disclaimer
Please ask your physician for a reliable diagnosis. This website is only meant as a reference.