Atrophodermia vermiculata L90.81

Sporadically occurring, chronic (harmless) disease pattern under several names. Clinically, in children and adolescents, the smallest wormlike, sharply retracted follicular scars (gaping follicles) with unknown etiology are found on the cheeks, usually symmetrically located on both sides. On close inspection, scattered follicular keratoses can often still be detected (see figure). The majority of authors interpret the clinical picture as a scarred final state of "atrophying" keratosis pilaris (faciei) (see also the explanations on the erythema perstans faciei).

Scarred final stage of an atrophying keratosis pilaris in the facial region. Sporadic occurrence. Gene locus (so far) not known.

Conspicuous in adolescence or early adulthood; no gender preference known.

Also occurs in Bazex-Dupré-Christol syndrome (back of the hand and foot).

Cheeks bds. mostly symmetrical distribution.

1. Scars after small lupus erythematosus chronicus dicoides
2. acne necrotica
3. Varicella scars
4. Comedon nevus

1. Chisholm C et al (2011) Unusual and recently described cutaneous atrophic disorders. Int J Dermatol 50:1506-151
2. The A, Podder I (2014) Atrophoderma vermiculatum. Indian Pediatr51:679
3. Darier J (1920) Atrophodermia vermiculée des joues avec kératoses follikulaires. Bull Soc Franc Derm Syph 27: 345
4. Jansen T et al (2003) Atrophodermia vermiculata: case report and review of the literature. J Eur Acad Dermatol Venereol 17:70-72
5. Schaller J et al (2010) Sweat duct proliferation associated with aggregates of elastic tissue and atrophodermia vermiculata: a simulator of microcystic adnexal carcinoma. Report of two cases. J Cutan catheter 37:1002-1009