Ainhum syndromeL94.6
Synonym(s)
Dactylosis spontanea
DefinitionThis section has been translated automatically.
Predominantly occurring in Africans, independent, clinically and radiologically definite, aetiologically unexplained, circular laceration of distal extremities with subsequent spontaneous amputation; usually lasting for years.
EtiopathogenesisThis section has been translated automatically.
Chronic trauma and infections (barefoot walk) as well as reduced blood supply are discussed; questionable relation to keratosis palmoplantaris mutilans (see Pseudoainhum syndrome).
ManifestationThis section has been translated automatically.
For people living in tropical regions, especially middle-aged Africans.
LocalizationThis section has been translated automatically.
Mainly metatarsophalangeal joint, usually on both sides.
Clinical featuresThis section has been translated automatically.
Circular, continuously deepening laceration, edema of the distal phalanges, finally dry gangrene and spontaneous amputation. Mostly a course lasting for years.
Differential diagnosisThis section has been translated automatically.
Pseudoainhum syndrome (congenital!)
TherapyThis section has been translated automatically.
Textile clothing, early professional wound treatment, plastic surgery reconstruction if necessary.
Note(s)This section has been translated automatically.
The term "Ainhum" comes from the African Yoruba dialect and means "saw, saw off".
Case report(s)This section has been translated automatically.
A 42-year-old African woman complained of painful fissures of the small toes. Clinical presentation showed edematous swelling of both end phalanges proximally limited by deep constrictions with hyperkeratosis, rhagades and linear indurations. The right distal phalanx showed no bony continuity and could be easily moved to and fro by dangling. Therapy: Partial amputation of the right small toe.
LiteratureThis section has been translated automatically.
- Castori M et al (2010) Palmoplantar keratoderma, pseudo-ainhum, and universal atrichia: Anew patient and review of the palmoplantar keratoderma-congenital alopecia syndrome. At J Med Genet A 152A: 2043-2047.
- Roesch A et al (2007) A patient with dangling toe. JDDG 11: 1008-1009
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Shtofmakher G et al (2014) Autoamputation of the fifth digit: ainhum (dactylolysis spontanea). BMJ Case Rep doi: 10.1136/bcr-2014-205021.