Synonym(s)
Acropathia ulcero-mutilans acquisita; Acropathia ulcero-mutilans et deformans pseudosyringomyelitica; Acropathia ulcero-mutilans et deformans pseudo-syringomyelitica; Acropathy non familial pseudosyringomyelitis ulcero-mutilating; Acropathy non familial syringomylie-like ulcero-mutilating; Bureau-Barrière syndrome; non-familial syringomyelia-like ulceromutilising acropathy; Syringomyelia-like ulceromutilating acropathy nonfamilial
HistoryThis section has been translated automatically.
Bureau and Barrière, 1955
DefinitionThis section has been translated automatically.
Non-familiar neurotrophic ulcerations and mutating acroosteolyses of the feet and hands, occurring in the context of a polyneuropathy (usually of ethyltoxic origin).
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EtiopathogenesisThis section has been translated automatically.
Unknown, provoking factor: chronic alcoholism, probably multifactorial.
ManifestationThis section has been translated automatically.
Mainly men between the ages of 40 and 50.
LocalizationThis section has been translated automatically.
Feet, mostly symmetrical.
Clinical featuresThis section has been translated automatically.
Deep, painless ulcerations with a hyperkeratotic border wall (see Collerette cornée). Stocking-like polyneuropathy, often with dissociated sensory disturbances. Non-reactive osteolysis of the loaded forefoot. Loss of thermal sensitivity, hyperhidrosis, lack of Achilles tendon reflex. Elephantiasis-like tissue hypertrophy, oedematous and verrucous changes, pachydermia, frequent recurrent erysipelas.
LaboratoryThis section has been translated automatically.
Anemia, dysproteinemia.
Differential diagnosisThis section has been translated automatically.
Acropathia ulcero-mutilans familiaris
Malum perforans (in diabetic polyneuropathy)
Pressure ulcers (painful, acute)
TherapyThis section has been translated automatically.
Treatment of accompanying diseases (e.g. alcoholism). Otherwise symptomatic in cooperation with internists and orthopaedic surgeons. Avoidance of permanent mechanical stimuli and pressure relief (orthopaedic footwear). In case of ulcers, early treatment of the wound according to its stage. In case of osseous destruction surgical intervention necessary.
LiteratureThis section has been translated automatically.
- Bureau Y, Barrière H (1955) Acropathies pseudo-syringo-myéliques des membres inférieurs. Essai d'interprétation nosographique. Sem Hôp Paris 31: 1419-1429
- Castle G, Castle D (1990) The Bureau-Barrière syndrome. Phlebol Proctol 19: 147-152
- Köhn FM et al (1991) Acroosteopathia ulceromutilans Bureau barrier. Act Dermatol 17: 39-42
- Preisz K et al (2002) Launois-Bensaude syndrome and Bureau-Barriere syndrome in a psoriatic patient: successful treatment with carbamazepine. Eur J Dermatol 12: 267-269
- Vanhooteghem O et al (1999) Acropathia ulcero-mutilans acquisita of the upper limbs. Br J Dermatol 140: 334-337
- Vogl A et al (2005) Skin and alcohol. J Dtsch Dermatol Ges 3: 788-790
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Incoming links (13)
Acroosteolysis; Acropathia ulcero-mutilans acquisita; Acropathia ulcero-mutilans et deformans pseudosyringomyelitica; Acropathia ulcero-mutilans et deformans pseudo-syringomyelitica; Acropathy, non familial syringomylie-like ulcero-mutilating; Acropathy, non-family pseudosyringomyelitic ulcero-mutilating; Bureau-barrière syndrome; Collerette cornée; Foot syndrome diabetic; Malum perforans; ... Show allOutgoing links (10)
Collerette cornée; Elephantiasis; Hyperhidrosis (overview); Hyperkeratoses; Malum perforans; Neuropathy, hereditary sensory and autonomic, type I; Pachydermia; Recurrent erysipelas; Ulcer of the skin (overview); Wound treatment;Disclaimer
Please ask your physician for a reliable diagnosis. This website is only meant as a reference.
Prof. Dr. med. Peter Altmeyer